Incontinentia pigmenti achromians (Ito) begins during childhood and is charac-terized by progressive appearance of bizarre patchy or whorl-like hypopigmentation without any preceeding or associated inflammatory changes in a fashion that resembles a negative picture of pigmentation in patients with incontinentia pigmenti. Mental, bony and ocular symptoms are not infrequently found in association with incontinentia pigmenti achromians. The incidence is high in the female sex, and there is no hereditary background.
A 24-year-old Korean soldier was first seen in May 1974 in dermatolbgic clinic of Capital Armed Forces General Hospital. Bizarre, reticulated, linear and whorl-like hypepigmented macular lesions were noted on the skin of the trunk and both extremities. The lesions started at the age of 4 year and developed without any inflammatory signs Family history did not disclose any type of pigmentation The disorder, and mental, bony and occular manifestations were not found.
biopsy specimen demonstrated that the amount of melanin in the basal layer was decreased in the hypopigmented area, and reveals neither inflammatory changes nor dropping off of melanin granules into the dermis.
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